Evaluation of Regorafenib in Newly Diagnosed and Recurrent Glioblastoma: GBM AGILE Phase II/III Bayesian Randomized Platform Trial

J James R. Perry (Sunnybrook Health Sciences Centre, University of Toronto, Toronto, Canada) E Emma Viktoria Hyddmark (Global Coalition for Adaptive Research, Larkspur, CA) T Timothy Cloughesy (University of California Los Angeles, Global Coalition for Adaptive Research, Los Angeles, CA) B Brian Alexander M Mark D. Anderson L Lars Anker D Donald A. Berry (Berry Consultants, LLC, Austin, TX) N Nicholas S. Berry (Berry Consultants, Austin, TX) N Nicholas A. Blondin (Yale University, New Haven, CT) O Omar H. Butt M Meredith B. Buxton (Global Coalition for Adaptive Research, Larkspur, CA) W Webster K. Cavenee (Department of Medicine, University of California at San Diego) T Tim Cloughesy H Howard Colman J Jennifer Connelly (1Medical College of Wisconsin, Milwaukee, United States) D Denise M. Damek (University of Colorado School of Medicine, Aurora, CO) J John de Groot (University of California San Francisco, San Francisco, CA) M Macarena I. De La Fuente M Michelle A. Detry (Berry Consultants, Austin, TX) J Jan Drappatz (22Department of Neurology and Medicine, University of Pittsburgh, Pittsburgh, PA) E Erin Dunbar (Piedmont Brain Tumor Center, Atlanta, GA) B Benjamin M. Ellingson M Mark Fitzgerald (Berry Consultants, Austin, TX) E Evanthia Galanis (Mayo Clinic, Rochester, MN) P Pierre Giglio (The Ohio State University Wexner Medical Center, Columbus, OH) G Gary Gordon J Jerome J. Graber T Todd L. Graves J Jethro Hu E Emma Maria Viktoria Hyddmark F Fabio Iwamoto (Columbia University Irving Medical Center, New York, NY) K Kurt A. Jaeckle (Mayo Clinic Florida, Jacksonville, FL) A Adam Johnson (Massachusetts General Hospital, Boston, Massachusetts, United States) M Marija Kalabic M Mustafa Khasraw L Lyndon Kim (Icahn School of Medicine at Mount Sinai, New York, NY) H Heather M. Kling (Global Coalition for Adaptive Research, Larkspur, CA) A Andrew B. Lassman (Division of Neuro-Oncology, Department of Neurology, Columbia University Vagelos College of Physicians and Surgeons, Herbert Irving Comprehensive Cancer Center, New York-Presbyterian, New York, NY) E Eudocia Q. Lee (Center for Neuro-Oncology, Dana-Farber Cancer Institute, Boston, MA) G Glenn J. Lesser M Michael Lim M Megan Mantica (University of Pittsburgh Medical Center, Pittsburgh, PA) J Joe Marion A Anna McGlothlin I Ingo Mellinghoff (3Memorial Sloan Kettering Cancer Center, New York, United States) T Tom Mikkelsen B Burt Nabors (University of Alabama at Birmingham, Birmingham, AL) H Herbert B. Newton (University Hospitals Cleveland Medical Center & Seidman Cancer Center, Cleveland, OH) J Jeffrey J. Olson (Emory University School of Medicine, Atlanta, GA) S Scott Owen (Department of Medical Oncology, McGill University Health Centre, Montreal) J James R Perry K Katherine B. Peters A Ashley Powell C Christina T. Saunders (Berry Consultants, Austin, TX) D David Schiff (31Department of Neurology, Division of Neuro-Oncology, University of Virginia, Charlottesville, VA) E Erik P. Sulman K Kirk Tanner S Sarah Untch T Tobias Walbert (Henry Ford Health, Michigan State and Wayne State University, Detroit, MI) S Shiao-Pei Weathers M Michael Weller P Patrick Y. Wen E Emma Wilcox W W. K. Alfred Yung

Abstract

PURPOSE GBM AGILE (ClinicalTrials.gov identifier: NCT03970447 ) is a phase II/III Bayesian adaptive platform registration trial testing multiple arms against a common control; the primary end point is overall survival (OS). Regorafenib, a multikinase inhibitor, showed OS benefit in recurrent (RD) glioblastoma in the phase II REGOMA trial and entered GBM AGILE as the first investigational arm. METHODS Patient subtypes included in the regorafenib arm of GBM AGILE were newly diagnosed unmethylated (NDU) and RD glioblastoma. Prospective defined sets of subtypes, or arm signatures, were NDU, RD, and all (NDU + RD). As the first investigational arm in GBM AGILE, regorafenib was equally randomized to the control arm. Treatment in the control arm is temozolomide + radiotherapy (in newly diagnosed) or lomustine (in RD). Efficacy was assessed by OS hazard ratio (HR), arm/control, and demonstrated when the Bayesian probability of benefit (HR <1.00) was ≥98%. Analysis was performed monthly for limited efficacy, which occurs when the Bayesian predictive power is <25% for all signatures, and determines stopping enrollment. Follow-up continued for 12 months after accrual stopped. RESULTS When the predictive power was <25% in all predefined signatures for regorafenib, accrual stopped for limited efficacy. The final analysis did not demonstrate OS improvement in the regorafenib arm in RD nor NDU glioblastoma. Median HRs were 1.05 (NDU), 1.07 (RD), and 1.07 (all) with final probabilities of benefit (HR <1.00) of 0.421 (NDU), 0.312 (RD), and 0.296 (all). Regorafenib was associated with increased toxicity relative to control. CONCLUSION GBM AGILE did not show superiority of regorafenib over control in RD (lomustine) or NDU (temozolomide + radiotherapy) glioblastoma, yet caused increased toxicities. Regorafenib has been removed from National Comprehensive Cancer Network guidelines as a treatment option for RD.

Article Details

Volume / Issue Vol. 44, Issue 18
Published June 20, 2026
Pages 1676-1686
ISSN 0732-183X
Publisher Lippincott Williams & Wilkins

Journal Info

Journal of Clinical Oncology

Lippincott Williams & Wilkins

ISSN: 0732-183X Health Sciences

Authors (64)

J

James R. Perry

Sunnybrook Health Sciences Centre, University of Toronto, Toronto, Canada

E

Emma Viktoria Hyddmark

Global Coalition for Adaptive Research, Larkspur, CA

T

Timothy Cloughesy

University of California Los Angeles, Global Coalition for Adaptive Research, Los Angeles, CA

B

Brian Alexander

M

Mark D. Anderson

L

Lars Anker

D

Donald A. Berry

Berry Consultants, LLC, Austin, TX

N

Nicholas S. Berry

Berry Consultants, Austin, TX

N

Nicholas A. Blondin

Yale University, New Haven, CT

O

Omar H. Butt

M

Meredith B. Buxton

Global Coalition for Adaptive Research, Larkspur, CA

W

Webster K. Cavenee

Department of Medicine, University of California at San Diego

T

Tim Cloughesy

H

Howard Colman

J

Jennifer Connelly

1Medical College of Wisconsin, Milwaukee, United States

D

Denise M. Damek

University of Colorado School of Medicine, Aurora, CO

J

John de Groot

University of California San Francisco, San Francisco, CA

M

Macarena I. De La Fuente

M

Michelle A. Detry

Berry Consultants, Austin, TX

J

Jan Drappatz

22Department of Neurology and Medicine, University of Pittsburgh, Pittsburgh, PA

E

Erin Dunbar

Piedmont Brain Tumor Center, Atlanta, GA

B

Benjamin M. Ellingson

M

Mark Fitzgerald

Berry Consultants, Austin, TX

E

Evanthia Galanis

Mayo Clinic, Rochester, MN

P

Pierre Giglio

The Ohio State University Wexner Medical Center, Columbus, OH

G

Gary Gordon

J

Jerome J. Graber

T

Todd L. Graves

J

Jethro Hu

E

Emma Maria Viktoria Hyddmark

F

Fabio Iwamoto

Columbia University Irving Medical Center, New York, NY

K

Kurt A. Jaeckle

Mayo Clinic Florida, Jacksonville, FL

A

Adam Johnson

Massachusetts General Hospital, Boston, Massachusetts, United States

M

Marija Kalabic

M

Mustafa Khasraw

L

Lyndon Kim

Icahn School of Medicine at Mount Sinai, New York, NY

H

Heather M. Kling

Global Coalition for Adaptive Research, Larkspur, CA

A

Andrew B. Lassman

Division of Neuro-Oncology, Department of Neurology, Columbia University Vagelos College of Physicians and Surgeons, Herbert Irving Comprehensive Cancer Center, New York-Presbyterian, New York, NY

E

Eudocia Q. Lee

Center for Neuro-Oncology, Dana-Farber Cancer Institute, Boston, MA

G

Glenn J. Lesser

M

Michael Lim

M

Megan Mantica

University of Pittsburgh Medical Center, Pittsburgh, PA

J

Joe Marion

A

Anna McGlothlin

I

Ingo Mellinghoff

3Memorial Sloan Kettering Cancer Center, New York, United States

T

Tom Mikkelsen

B

Burt Nabors

University of Alabama at Birmingham, Birmingham, AL

H

Herbert B. Newton

University Hospitals Cleveland Medical Center & Seidman Cancer Center, Cleveland, OH

J

Jeffrey J. Olson

Emory University School of Medicine, Atlanta, GA

S

Scott Owen

Department of Medical Oncology, McGill University Health Centre, Montreal

J

James R Perry

K

Katherine B. Peters

A

Ashley Powell

C

Christina T. Saunders

Berry Consultants, Austin, TX

D

David Schiff

31Department of Neurology, Division of Neuro-Oncology, University of Virginia, Charlottesville, VA

E

Erik P. Sulman

K

Kirk Tanner

S

Sarah Untch

T

Tobias Walbert

Henry Ford Health, Michigan State and Wayne State University, Detroit, MI

S

Shiao-Pei Weathers

M

Michael Weller

P

Patrick Y. Wen

E

Emma Wilcox

W

W. K. Alfred Yung