<i>NOTCH1</i> Mutation and Survival Analysis of Tislelizumab in Advanced or Metastatic Esophageal Squamous Cell Carcinoma: A Biomarker Analysis From the Randomized, Phase III, RATIONALE-302 Trial

Z Zhihao Lu (Key Laboratory of Life‐Organic Analysis of Shandong Province School of Chemistry and Chemical Engineering Qufu Normal University Qufu 273165 P.R. China) W Wenting Du (Zhihao Lu, MD, Department of Gastrointestinal Oncology, Key Laboratory of Carcinogenesis and Translational Research (Ministry of Education), Peking University Cancer Hospital &amp; Institute, Beijing, China; Wenting Du, PhD, Clinical Biomarker, BeOne Medicines, Ltd, Shanghai, China; Xi Jiao, MD, and Yanni Wang, PhD, Department of Gastrointestinal Oncology, Key Laboratory of Carcinogenesis and Translational Research (Ministry of Education), Peking University Cancer Hospital &amp; Institute, Beijing, China; Zhang Zhang, PhD, Statistics, BeOne Medicines, Ltd, Beijing, China; and Lin Shen, MD, Department of Gastrointestinal Oncology, Key Laboratory of Carcinogenesis and Translational Research (Ministry of Education), Peking University Cancer Hospital &amp; Institute, Beijing, China, State Key Laboratory of Holistic Integrative Management of Gastrointestinal Cancers, Beijing Key Laboratory of Carcinogenesis and Translational Research, Department of Gastrointestinal Oncology, Peking University Cancer Hospital &a...) X Xi Jiao (Zhihao Lu, MD, Department of Gastrointestinal Oncology, Key Laboratory of Carcinogenesis and Translational Research (Ministry of Education), Peking University Cancer Hospital &amp; Institute, Beijing, China; Wenting Du, PhD, Clinical Biomarker, BeOne Medicines, Ltd, Shanghai, China; Xi Jiao, MD, and Yanni Wang, PhD, Department of Gastrointestinal Oncology, Key Laboratory of Carcinogenesis and Translational Research (Ministry of Education), Peking University Cancer Hospital &amp; Institute, Beijing, China; Zhang Zhang, PhD, Statistics, BeOne Medicines, Ltd, Beijing, China; and Lin Shen, MD, Department of Gastrointestinal Oncology, Key Laboratory of Carcinogenesis and Translational Research (Ministry of Education), Peking University Cancer Hospital &amp; Institute, Beijing, China, State Key Laboratory of Holistic Integrative Management of Gastrointestinal Cancers, Beijing Key Laboratory of Carcinogenesis and Translational Research, Department of Gastrointestinal Oncology, Peking University Cancer Hospital &a...) Y Yanni Wang J Jingwen Shi Y Yang Shi Y Yongqian Shu (Jiangsu Province Hospital, Nanjing, China) Z Zuoxing Niu H Hiroki Hara (Saitama Cancer Center, Ina, Japan) J Jun Wu C Chih-Hung Hsu (National Taiwan University Cancer Center, Taipei City, Taiwan) E Eric Van Cutsem (University Hospitals Gasthuisberg, Leuven, Belgium) M Malcolm V. Brock Z Zhang Zhang (State Key Laboratory of Bioactive Molecules and Druggability Assessment, and School of Pharmacy, Jinan University, 601 Huangpu Avenue West, Guangzhou 510632, China) N Ningning Ding (Clinical Development, BeiGene (Beijing) Co, Ltd, Beijing, China) Y Yun Zhang Z Zhirong Shen (20BeOne Medicines Ltd, Shanghai, China) L Lin Shen

Abstract

PURPOSE Although multiple agents targeting PD-1 have been approved as second-line treatment for esophageal squamous cell carcinoma (ESCC), only a fraction of patients derive long-term survival. Hence, reliable predictive biomarkers are urgently needed. METHODS Comprehensive tumor genomic profiling and transcriptome sequencing were performed on samples from the RATIONALE-302 study. We also conducted single-cell RNA sequencing analysis on Notch1 knockdown ESCC murine models to further explore the potential molecular mechanisms underlying anti–PD-1 benefit. RESULTS We identified NOTCH1 mutation as a potential predictive biomarker for longer overall survival (OS) with tislelizumab versus chemotherapy (18.4 months v 5.3 months; hazard ratio, 0.35 [95% CI, 0.17 to 0.71]). At the transcriptional level, type I IFN (IFN-I)/toll-like receptor expression signatures were positively associated with OS benefit of tislelizumab, whereas B-cell and neutrophil signatures predicted unfavorable OS. Exploratory analyses showed that the presence of NOTCH1 mutation correlated with enrichment of IFN-I signatures and reduced infiltration of B cells and neutrophils. In murine models, comparative single-cell transcriptome analyses further revealed that Notch1 deficiency facilitated a more immunologically activated tumor microenvironment which potentiated anti–PD-1 treatment. CONCLUSION Our data provide novel insights for anti–PD-1 treatment selection using NOTCH1 mutations and may provide a rationale for combination therapy in ESCC.

Article Details

Volume / Issue Vol. 43, Issue 16
Published June 01, 2025
Pages 1898-1909
ISSN 0732-183X
Publisher Lippincott Williams & Wilkins

Journal Info

Journal of Clinical Oncology

Lippincott Williams & Wilkins

ISSN: 0732-183X Health Sciences

Authors (18)

Z

Zhihao Lu

Key Laboratory of Life‐Organic Analysis of Shandong Province School of Chemistry and Chemical Engineering Qufu Normal University Qufu 273165 P.R. China

W

Wenting Du

Zhihao Lu, MD, Department of Gastrointestinal Oncology, Key Laboratory of Carcinogenesis and Translational Research (Ministry of Education), Peking University Cancer Hospital &amp; Institute, Beijing, China; Wenting Du, PhD, Clinical Biomarker, BeOne Medicines, Ltd, Shanghai, China; Xi Jiao, MD, and Yanni Wang, PhD, Department of Gastrointestinal Oncology, Key Laboratory of Carcinogenesis and Translational Research (Ministry of Education), Peking University Cancer Hospital &amp; Institute, Beijing, China; Zhang Zhang, PhD, Statistics, BeOne Medicines, Ltd, Beijing, China; and Lin Shen, MD, Department of Gastrointestinal Oncology, Key Laboratory of Carcinogenesis and Translational Research (Ministry of Education), Peking University Cancer Hospital &amp; Institute, Beijing, China, State Key Laboratory of Holistic Integrative Management of Gastrointestinal Cancers, Beijing Key Laboratory of Carcinogenesis and Translational Research, Department of Gastrointestinal Oncology, Peking University Cancer Hospital &a...

X

Xi Jiao

Zhihao Lu, MD, Department of Gastrointestinal Oncology, Key Laboratory of Carcinogenesis and Translational Research (Ministry of Education), Peking University Cancer Hospital &amp; Institute, Beijing, China; Wenting Du, PhD, Clinical Biomarker, BeOne Medicines, Ltd, Shanghai, China; Xi Jiao, MD, and Yanni Wang, PhD, Department of Gastrointestinal Oncology, Key Laboratory of Carcinogenesis and Translational Research (Ministry of Education), Peking University Cancer Hospital &amp; Institute, Beijing, China; Zhang Zhang, PhD, Statistics, BeOne Medicines, Ltd, Beijing, China; and Lin Shen, MD, Department of Gastrointestinal Oncology, Key Laboratory of Carcinogenesis and Translational Research (Ministry of Education), Peking University Cancer Hospital &amp; Institute, Beijing, China, State Key Laboratory of Holistic Integrative Management of Gastrointestinal Cancers, Beijing Key Laboratory of Carcinogenesis and Translational Research, Department of Gastrointestinal Oncology, Peking University Cancer Hospital &a...

Y

Yanni Wang

J

Jingwen Shi

Y

Yang Shi

Y

Yongqian Shu

Jiangsu Province Hospital, Nanjing, China

Z

Zuoxing Niu

H

Hiroki Hara

Saitama Cancer Center, Ina, Japan

J

Jun Wu

C

Chih-Hung Hsu

National Taiwan University Cancer Center, Taipei City, Taiwan

E

Eric Van Cutsem

University Hospitals Gasthuisberg, Leuven, Belgium

M

Malcolm V. Brock

Z

Zhang Zhang

State Key Laboratory of Bioactive Molecules and Druggability Assessment, and School of Pharmacy, Jinan University, 601 Huangpu Avenue West, Guangzhou 510632, China

N

Ningning Ding

Clinical Development, BeiGene (Beijing) Co, Ltd, Beijing, China

Y

Yun Zhang

Z

Zhirong Shen

20BeOne Medicines Ltd, Shanghai, China

L

Lin Shen