Phase I Study of <sup>131</sup> I-Metaiodobenzylguanidine With Dinutuximab ± Vorinostat for Patients With Relapsed or Refractory Neuroblastoma: A New Approaches to Neuroblastoma Therapy Trial

T Thomas Cash (Aflac Cancer &amp; Blood Disorders Center, Children's Healthcare of Atlanta, Emory University School of Medicine, Atlanta, GA) A Araz Marachelian (Cancer and Blood Disease Institute, Children's Hospital Los Angeles; Keck School of Medicine, University of Southern California, Los Angeles, CA) S Steven G. DuBois Y Yueh-Yun Chi (3Division of Hematology, Oncology and Blood and Marrow Transplant, Children's Hospital Los Angeles, Los Angeles, United States) A Anahit Baregamyan (Children's Hospital Los Angeles; Keck School of Medicine, University of Southern California, Los Angeles, CA) S Susan G. Groshen (USC Norris Comprehensive Cancer Center, Los Angeles, CA) H Hunter C. Jonus (Department of Pediatrics, Aflac Cancer and Blood Disorders Center, Children's Healthcare of Atlanta, Emory University School of Medicine, Atlanta, GA) A Anasheh Shamirian (Department of Pediatrics, Children's Hospital Los Angeles, Keck School of Medicine, University of Southern California, Los Angeles, CA) M Mary Crowley (Department of Pediatrics, Children's Hospital Los Angeles, Keck School of Medicine, University of Southern California, Los Angeles, CA) F Fariba Goodarzian (Children's Hospital Los Angeles; Keck School of Medicine, University of Southern California, Los Angeles, CA) P Patricia T. Acharya (Department of Radiology, Children's Hospital Los Angeles, Keck School of Medicine, University of Southern California, Los Angeles, CA) B Bruce Pawel (Children's Hospital Los Angeles; Keck School of Medicine, University of Southern California, Los Angeles, CA) A Amy K. Erbe A Ankita Shahi (Hematology/ Oncology School of Medicine and Public Health, University of Wisconsin, Madison, WI) J Jen Zaborek (Departments of Pediatrics, Human Oncology, or Biostatistics, University of Wisconsin-Madison School of Medicine and Public Health, Madison, WI) E Eleanor Kennedy (Departments of Pediatrics, Human Oncology, or Biostatistics, University of Wisconsin-Madison School of Medicine and Public Health, Madison, WI) S Shahab Asgharzadeh (Cancer and Blood Disease Institute Children's Hospital Los Angeles 4650 Sunset Blvd Los Angeles California 90027 USA) J Judith G. Villablanca (Department of Pediatrics, Children's Hospital Los Angeles, Keck School of Medicine, University of Southern California, Los Angeles, CA) N Navin Pinto (1University of Colorado School of Medicine, Aurora, United States) B Brian D. Weiss (Department of Pediatrics, Division of Oncology, Cincinnati Children's Hospital Medical Center, Cincinnati, OH) Y Yael P. Mossé A Ami V. Desai (Department of Pediatrics, University of Chicago, Chicago, IL) M Margaret E. Macy (Department of Pediatrics, University of Colorado and Center for Cancer and Blood Disorders, Children’s Hospital Colorado, Aurora, CO) M Meaghan Granger (Cook Children's Medical Center, Fort Worth, TX) K Kieuhoa T. Vo (Department of Pediatrics, UCSF Benioff Children's Hospital, University of California San Francisco School of Medicine, San Francisco, CA) P Paul M. Sondel K Katherine K. Matthay (Department of Pediatrics, UCSF Benioff Children's Hospital, University of California San Francisco School of Medicine, San Francisco, CA) J Julie R. Park K Kelly C. Goldsmith (Department of Pediatrics, Aflac Cancer and Blood Disorders Center, Children's Healthcare of Atlanta, Emory University School of Medicine, Atlanta, GA)

Abstract

PURPOSE We conducted a phase I trial to determine the safety, tolerability, and preliminary antitumor activity of 131 I-metaiodobenzylguanidine (MIBG) combined with the anti-GD2 antibody dinutuximab with or without the histone deacetylase inhibitor vorinostat in patients with relapsed/refractory neuroblastoma (rNBL). METHODS In part A, patients with MIBG-avid rNBL received MIBG intravenously (IV) on day 1 at 12, 15, or 18 mCi/kg per the rolling six design and dinutuximab (17.5 mg/m 2 once daily) IV on days 8-11 and 29-32 and granulocyte-macrophage colony-stimulating factor (250 mcg/m 2 once daily) subcutaneously on days 8-17 and 29-38. Autologous stem cells were infused on day 15. In part B, vorinostat at 180 mg/m 2 once daily was given orally on days 0-13 in combination with the part A recommended phase II dose (RP2D). Patients could receive two courses. RESULTS Forty-five eligible patients enrolled, of whom 31 were evaluable. The median age was 7.5 (range, 2.9-24.1) years. For part A (n = 19), no dose-limiting toxicities (DLTs) occurred across all dose levels and courses, establishing the RP2D of MIBG to be 18 mCi/kg. In part B (n = 12), 1 DLT (grade 3 hypokalemia) occurred during course 1, and 3 of 11 patients who received a second course experienced DLT: grade 3 ALT increase, grade 4 hypoxia and grade 5 pneumonitis, and grade 3 fatigue. The best overall response rate (BORR; complete response [CR] + partial response [PR]) on part A was 42% with a CR/PR/minor response (MR) rate of 46%, and 19% progressive disease (PD) rate. For part B, the BORR was 42% with a CR/PR/MR rate of 75% and 0% PD rate. CONCLUSION MIBG combined with dinutuximab was well tolerated with encouraging antitumor activity. Vorinostat added to this combination may augment responses in this heavily pretreated patient population.

Article Details

Volume / Issue Vol. 43, Issue 22
Published August 01, 2025
Pages 2490-2501
ISSN 0732-183X
Publisher Lippincott Williams & Wilkins

Journal Info

Journal of Clinical Oncology

Lippincott Williams & Wilkins

ISSN: 0732-183X Health Sciences

Authors (29)

T

Thomas Cash

Aflac Cancer &amp; Blood Disorders Center, Children's Healthcare of Atlanta, Emory University School of Medicine, Atlanta, GA

A

Araz Marachelian

Cancer and Blood Disease Institute, Children's Hospital Los Angeles; Keck School of Medicine, University of Southern California, Los Angeles, CA

S

Steven G. DuBois

Y

Yueh-Yun Chi

3Division of Hematology, Oncology and Blood and Marrow Transplant, Children's Hospital Los Angeles, Los Angeles, United States

A

Anahit Baregamyan

Children's Hospital Los Angeles; Keck School of Medicine, University of Southern California, Los Angeles, CA

S

Susan G. Groshen

USC Norris Comprehensive Cancer Center, Los Angeles, CA

H

Hunter C. Jonus

Department of Pediatrics, Aflac Cancer and Blood Disorders Center, Children's Healthcare of Atlanta, Emory University School of Medicine, Atlanta, GA

A

Anasheh Shamirian

Department of Pediatrics, Children's Hospital Los Angeles, Keck School of Medicine, University of Southern California, Los Angeles, CA

M

Mary Crowley

Department of Pediatrics, Children's Hospital Los Angeles, Keck School of Medicine, University of Southern California, Los Angeles, CA

F

Fariba Goodarzian

Children's Hospital Los Angeles; Keck School of Medicine, University of Southern California, Los Angeles, CA

P

Patricia T. Acharya

Department of Radiology, Children's Hospital Los Angeles, Keck School of Medicine, University of Southern California, Los Angeles, CA

B

Bruce Pawel

Children's Hospital Los Angeles; Keck School of Medicine, University of Southern California, Los Angeles, CA

A

Amy K. Erbe

A

Ankita Shahi

Hematology/ Oncology School of Medicine and Public Health, University of Wisconsin, Madison, WI

J

Jen Zaborek

Departments of Pediatrics, Human Oncology, or Biostatistics, University of Wisconsin-Madison School of Medicine and Public Health, Madison, WI

E

Eleanor Kennedy

Departments of Pediatrics, Human Oncology, or Biostatistics, University of Wisconsin-Madison School of Medicine and Public Health, Madison, WI

S

Shahab Asgharzadeh

Cancer and Blood Disease Institute Children's Hospital Los Angeles 4650 Sunset Blvd Los Angeles California 90027 USA

J

Judith G. Villablanca

Department of Pediatrics, Children's Hospital Los Angeles, Keck School of Medicine, University of Southern California, Los Angeles, CA

N

Navin Pinto

1University of Colorado School of Medicine, Aurora, United States

B

Brian D. Weiss

Department of Pediatrics, Division of Oncology, Cincinnati Children's Hospital Medical Center, Cincinnati, OH

Y

Yael P. Mossé

A

Ami V. Desai

Department of Pediatrics, University of Chicago, Chicago, IL

M

Margaret E. Macy

Department of Pediatrics, University of Colorado and Center for Cancer and Blood Disorders, Children’s Hospital Colorado, Aurora, CO

M

Meaghan Granger

Cook Children's Medical Center, Fort Worth, TX

K

Kieuhoa T. Vo

Department of Pediatrics, UCSF Benioff Children's Hospital, University of California San Francisco School of Medicine, San Francisco, CA

P

Paul M. Sondel

K

Katherine K. Matthay

Department of Pediatrics, UCSF Benioff Children's Hospital, University of California San Francisco School of Medicine, San Francisco, CA

J

Julie R. Park

K

Kelly C. Goldsmith

Department of Pediatrics, Aflac Cancer and Blood Disorders Center, Children's Healthcare of Atlanta, Emory University School of Medicine, Atlanta, GA